섬유형성이상 환자의 눈 소견

• 영문명: Ocular Findings in Patients with Fibrous Dysplasia
• 발행기관: 대한안과학회
• 저자명: 김남주 왕규창 김석화 손우길 황정민,Nam Ju Kim, M.D., Kyu Chang Wang, M.D., Suk Wha Kim, M.D., Woo Gil Son, M.D., Jeong-Min Hwang, M.D.
• 간행물 정보: 『대한안과학회지』Ophthalmological Society,volume47,number5, 787~798쪽, 전체 12쪽
• 주제분류: 의약학 > 기타의약학
• 파일형태: PDF
• 발행일자: 2006.05.31

영문 초록

Purpose: Fibrous dysplasia is an uncommon disease that replaces normal bone tissue with fibrous and osteoid tissue. We evaluated patients with fibrous dysplasia involving orbital bones to identify the ocular characteristic findings. Methods: We recruited 6 patients with fibrous dysplasia of the craniofacial bone. Best corrected visual acuity and facial asymmetry were measured. Slit lamp biomicroscopy, tonometry, strabismus examination, and funduscopy were performed. Results: Strabismus, exophthalmos and optic neuropathy were found in 5, 4, and 2 patients, respectively. One patient underwent a strabismus surgery. One patient had McCune-Albright syndrome, exhibiting a caf?-au-lait spot of the skin and precocious puberty. All 6 patients had facial asymmetry and higher superior orbital rims of the affected side in 5 patients. Conclusions: Ophthalmologic examination may be mandatory for patients with fibrous dysplasia involving the orbit, especially to prevent optic neuropathy. If optic atrophy, strabismus or exophthalmos is found in patients with facial asymmetry, the possibility of fibrous dysplasia must be considered.

키워드

Fibrous dysplasia, Optic atrophy, Strabismus