내경동맥 협착이 동반된 비전형적 Miller-Fisher 증후군 1례 (Atypical Miller-Fisher Syndrome)

• 영문명: A Case of Atypical Miller-Fisher Syndrome with Internal Carotid Artery Stenosis
• 발행기관: 대한소아신경학회
• 저자명: 진지훈(Ji Hoon Jin) 최은혜(Eun Hye Choi) 조성대(Sung Dae Cho) 손병관(Byong Kwan Son) 강성모(Sung Mo Kang) 권영세(Yung Se Kwon)
• 간행물 정보: 『Annals of Child Neurology(구 대한소아신경학회지)』대한소아신경학회지 제18권 제2호, 311~316쪽, 전체 6쪽
• 주제분류: 의약학 > 소아과학
• 파일형태: PDF
• 발행일자: 2010.11.30

영문 초록

Miller-Fisher syndrome is an acute poly-neuropathy typically characterized by the triad of ophthalmoplegia, ataxia, and areflexia. Other poly-neuropathy diseases include Guillain-Barre syndrome and Bickerstaff brainstem encephalitis. However, not all cases of Miller-Fisher syndrome have the typical three symptoms. These diseases have been differentiated by clinical manifestations and anti-GQ1b IgG anti- body testing. In Miller-Fisher syndrome, anti-GQ1b IgG antibody is present in over 95% of patients; however, the frequency is not so high in normal subjects or in those with other poly-neuropathy diseases. Infectious illnesses, such as respiratory dis- eases and gastrointestinal diseases, usually precede Miller-Fisher syndrome. In ge- neral, Miller-Fisher syndrome is a self-limiting illness; however, a few cases of Miller-Fisher syndrome progressing to respiratory failure have been reported, parti- cularly in children. In this case, we report abnormal angiographic findings. We report a case of aty- pical Miller-Fisher syndrome with internal carotid artery stenosis treated with pred- nisolone.

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키워드

Miller Fisher Syndrome Polyneuropathies Child Vascular stenosis