혈전성 혈소판감소성 자반증으로 발현된 전신홍반루푸스 1예

• 영문명: Systemic Lupus Eiythematosus Presenting as Thromobotic Thrombocytopenic Puipura -A Case Report-
• 발행기관: 조선대학교 의학연구원
• 저자명: 오명근(Myueng-Guen Oh) 유미라(Mi-Ra You) 변유미(Yu-Mi Byeon) 윤찬영(Chan-Young Yun) 권세훈(Se-Hun Kwan) 박치영(Chi-You
• 간행물 정보: 『The Medical Journal of Chosun University』제32권 제3호, 88~93쪽, 전체 6쪽
• 주제분류: 의약학 > 기타의약학
• 파일형태: PDF
• 발행일자: 2007.10.31

영문 초록

Thrombotic thrombocytopenic purpura (TTP) is a life-threatening syndrome characterized by the classic pentad of clinical features that includes microangiopathic hemolytic anemia, thrombocytopenia, neurologic abnormalities, fever, and renal dysfunction. Early diagnosis and utilization of plasmapheresis can improve the survival rates of patients with TTP. TTP rarely may be seen in association with autoimmune disease such as systemic lupus erythematous (SLE). We report here a 42-year-old female who was presented with severe digital gangrenes, microangiopathic hemolytic anemia, thrombocytopenia, neurologic abnormalities, fever, and renal dysfunction. Her condition responded to combined therapy with high dose steroid, immunosuppressants, and plasmapheresis therapy.

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키워드

Systemic lupus erythematosus Lymphadenopathy Thromobotic thrombocytopenic purpura Plasmapheresis