A Case of Alveolar Rhabdomyosarcoma of the Ethmoid Sinus Invading the Orbit in an Adult

• 발행기관: 대한안과학회
• 저자명: Hyun Seung Moon Sang Won Kwon Jong Hyeok Lee
• 간행물 정보: 『The Korean Journal of Ophthalmology』Vol.20 No.1, 70~75쪽, 전체 6쪽
• 주제분류: 의약학 > 기타의약학
• 파일형태: PDF
• 발행일자: 2006.03.30

영문 초록

Purpose: A case study and literature review of alveolar rhabdomyosarcoma (RMS) in an adult. Methods: A 48-year-old male patient presented at our clinic complaining of proptosis that had persisted for 2 weeks in his left eye. A computed tomography (CT) scan revealed a destructive soft-tissue mass in the eft ethmoid sinus with invasion of the left orbit and compression of the medial rectus muscle. Endoscopic intranasal biopsy revealed alveolar RMS. Conservative debulking and orbital wall decompression were performed. Results: Immunohistochemical testing was positive for desmin, S-100, and smooth muscle actin (SMA), supporting the diagnosis of RMS. Since ipsilateral cervical and spinal metastasis was detected, systemic treatment was administered simultaneously. Conclusions: Although rarely found in adults, RMS should be considered in the differential diagnosis of orbital tumors. Immunohistochemical analysis plays an important role in the definitive diagnosis of RMS. Korean Journal of Ophthalmology 20(1):70-75, 2006

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Case Report

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키워드

Adult rhabdomyosarcoma Ethmoid Orbital tumor