시신경을 침범한 IgG4 연관 경화성 질환 1예

• 영문명: A Case of IgG4-Related Sclerosing Disease Involving the Optic Nerve
• 발행기관: 대한안과학회
• 저자명: 조형석 최정열 염정훈,Hyung Seok Cho, MD, Jung Yeol Choi, MD, Jung Hoon Yum, MD
• 간행물 정보: 『대한안과학회지』Ophthalmological Society,volume53,number12, 1879~1884쪽, 전체 6쪽
• 주제분류: 의약학 > 기타의약학
• 파일형태: PDF
• 발행일자: 2012.12.15

영문 초록

Purpose: To report a case of IgG4-related sclerosing dacryoadenitis masquerading for a long period as a. Case summary: A 59-year-old man with visual acuity loss and proptosis in the left eye was referred to our hospital. Ten years prior, the patient was diagnosed with lymphoma and underwent chemotherapy at another hospital. However, the patient spontaneously stopped treatment and took steroids for the relief of periorbital swelling. Magnetic resonance imaging revealed diffuse infiltrative lesions involving both optic nerves and extraocular muscles. Incisional biopsies of the lacrimal gland’s posterior side and the lateral rectus muscle’s lateral side were performed. Staining for IgG4 via immunochemistry showed infiltration of IgG4-positive lymphoplasmacytic cells. Under the diagnosis of IgG4-related sclerosing disease, the patient underwent high-dose steroid pulse therapy.

키워드

IgG4-related sclerosing disease, Mikulicz disease, Orbital inflammatory disease