안와와 안구표면을 동시에 침범한 신경섬유종증 1예

• 영문명: A Case of Neurofibromatosis of the Orbit and Ocular Surface
• 발행기관: 대한안과학회
• 저자명: 이광훈 박진우 윤경철,Kwang Hoon Lee, M.D., Jin Woo Park, M.D., Kyung Chul Yoon, M.D., Ph.D.
• 간행물 정보: 『대한안과학회지』Ophthalmological Society,volume48,number9, 1276~1280쪽, 전체 5쪽
• 주제분류: 의약학 > 기타의약학
• 파일형태: PDF
• 발행일자: 2007.09.30

영문 초록

Purpose: To report a case of neurofibromatosis of the orbit and ocular surface. Methods: A 26-year-old man was admitted complaining of conjunctival mass and exophthalmos. Lisch nodules on the iris were observed in the right eye, and corneal opacity with neovascularization and conjunctival mass were detected in the left eye. Orbital computed tomography revealed diffuse infiltrating facial tumors including the left orbit, suggestive of plexiform neurofibromatosis. Results: We performed evisceration of the left eye and excision of the left orbital mass. Histopathologic examination revealed neurofibroma which was positive for S-100. No recurrence was detected during a 6-month post-operative period.

키워드

Lisch Nodule, Orbital Neurofibromatosis