양안 수직근육전이술로 치유된 양안 듀안안구후퇴증후군 1예

• 영문명: Bilateral Duane’s Retraction Syndrome Treated with Bilateral Horizontal Transposition of Vertical Recti
• 발행기관: 대한안과학회
• 저자명: 조윤애 오인경,Yoonae A. Cho, M.D., Ph.D., In Kyung Oh, M.D.
• 간행물 정보: 『대한안과학회지』Ophthalmological Society,volume47,number6, 1016~1020쪽, 전체 5쪽
• 주제분류: 의약학 > 기타의약학
• 파일형태: PDF
• 발행일자: 2006.06.30

영문 초록

Purpose: To report a male infant with bilateral Duane`s retraction syndrome treated with bilateral horizontal transpositions of vertical recti to the lateral rectus muscle. Methods: An 8-month-old boy showed bilateral Duane`s retraction syndrome with esotropia of 45PD, severe limitation of abduction (-4 and -3.5 in each eye) and mild globe retraction in both eyes. It was assumed that he inherited the condition from his father through an autosomal dominant pattern. His father showed esotropia of 25PD with -4 limitation of abduction in the left eye and a left head-turn of 10。. He also had +2 globe retraction, +1 upshoot and +2 downshoot in adduction of the left eye. Transposition of two vertical recti to the lateral rectus muscle was performed in both eyes of the boy. Results: Nine months after surgery, the boy had achieved a microesotropia of 6PD in primary gaze with stereopsis of 3000 seconds of arc and considerable improvement in abduction (-2, -1.5 in each eye). The amount of correction of esodeviation was 39PD. This favorable state was maintained at follow-up 3.5 years after surgery. Conclusions: An 8-month-old boy who had esotropia of 45PD caused by bilateral Duane`s retraction syndrome, underwent bilateral horizontal transpositions of vertical recti to the lateral rectus muscle. He achieved a microesotropia of 6PD in primary gaze and considerable improvement of abduction with only mild eyeball retraction.

키워드

Autosomal dominant inheritance, Bilateral Duane`s retraction syndrome, Bilateral horizontal transpositions of vertical recti, Esotropia