색소성 융기성 피부섬유육종(Pigmented Dermatofibrosarcoma protuberans)의 치험례

• 영문명: A case report of pigmented dermatofibrosarcoma protuberans (Bednar tumor)
• 발행기관: 대한구강악안면외과학회
• 저자명: 이정삼(Jeong Sam Lee) 김건중(Kean Jung Kim) 정종철(Jong Cheol Jeong) 민홍기(Heung Ki Min) 최재선(Jae Sun Choi) 박홈례(Heum Rye Park) 박성혜(Sung Hye Park) 하승연(Seung Yon Ha)
• 간행물 정보: 『대한구강악안면외과학회지』대한구강악안면외과학회지 제23권 제1호, 145~151쪽, 전체 7쪽
• 주제분류: 의약학 > 내과학
• 파일형태: PDF
• 발행일자: 1997.01.30

영문 초록

Bednar tumor was described by Bednar in 1957. The histologic pattern of this tumor shows similar to dermatofibrosarcoma protuberans (DFSP) but melanin pigments are scattered within the tumor, It s rare neoplasm accounting for approximately 1-5% of all case of DFSP. Clinically, this tumor is considered to be intermediated malignancy, because of slow growth and frequent local recurrence and lack of distant metastasis. The majority are located on the trunk and the upper and lower extremities, but extremely rate in the head and neck area. Microscopically, this tumor is characterized by tight storiform spindle cells and long slender cells that admixed with a small population of melanin containing dendritic cells. This dendritic cells are the primary features distinguising this lesion from conventional DFSP. Complete surgical excision and close follow-up case are necessany for this neoplasm because of probable intermediate malignancy. A patient was admitted to Our Department of Oral and Maxillofacial Surgery due to swelling on right parotid area and numbness of the right lower lip on September, 1994, By clinical examinations and C-T finding, we dignosed tentatively as myxoma or pleomorphic adenoma. Surgical excision of this tumor was performed with parotidectomy and mandibular osteotomy under the frozen biopsy. By final microscopic and electromicroscopic examination and immunohistochemical study, this tumor was diagnosed as Bednar tumor. So, we report a case of pigmented DFSP with review of literatures.

목차

Abstract

I. 서론

II. 증례보고

III. 고찰

IV. 요약

REFERANCES

키워드

Pigmented dermatofibrosarcoma protuberans Melanin pigments